Code browser

15675 searchable codes: 15573 in the ICD-10-CA release, the 74 withdrawn in it, and the crosswalk codes that exist only in ICD-10-CM. Filter by specialty, diagnostic category, body system, coding standard, chapter and reportability. 1569 are linked to a structure in the 3D explorer.

About the facets. Diagnostic category and body system are derived by this service from the published chapter and block structure — C00–D48 is neoplasm wherever it appears, C64–C68 is urinary tract. They are search aids, not CIHI's editorial assignment, and carry no authority for a coding decision. Codes bound to anatomy use their real mapping instead of the derived one.

453 codes · page 8 of 10

E723 ICD-10-CA

Disorders of lysine and hydroxylysine metabolism

Chapter IV · subcategory · degenerative * · ICD-10-CA

E724 ICD-10-CA

Disorders of ornithine metabolism

Chapter IV · subcategory · degenerative * · ICD-10-CA

E725 ICD-10-CA

Disorders of glycine metabolism

Chapter IV · subcategory · degenerative * · ICD-10-CA

E728 ICD-10-CA

Other specified disorders of amino-acid metabolism

Chapter IV · subcategory · degenerative * · ICD-10-CA

E729 ICD-10-CA

Disorder of amino-acid metabolism, unspecified

Chapter IV · subcategory · degenerative * · ICD-10-CA

E730 ICD-10-CA

Congenital lactase deficiency

Chapter IV · subcategory · degenerative * · ICD-10-CA

E731 ICD-10-CA

Secondary lactase deficiency

Chapter IV · subcategory · degenerative * · ICD-10-CA

E738 ICD-10-CA

Other lactose intolerance

Chapter IV · subcategory · degenerative * · ICD-10-CA

E739 ICD-10-CA

Lactose intolerance, unspecified

Chapter IV · subcategory · degenerative * · ICD-10-CA

E740 ICD-10-CA

Glycogen storage disease

Chapter IV · subcategory · degenerative * · ICD-10-CA

E741 ICD-10-CA

Disorders of fructose metabolism

Chapter IV · subcategory · degenerative * · ICD-10-CA

E742 ICD-10-CA

Disorders of galactose metabolism

Chapter IV · subcategory · degenerative * · ICD-10-CA

E743 ICD-10-CA

Other disorders of intestinal carbohydrate absorption

Chapter IV · subcategory · degenerative * · ICD-10-CA

E744 ICD-10-CA

Disorders of pyruvate metabolism and gluconeogenesis

Chapter IV · subcategory · degenerative * · ICD-10-CA

E748 ICD-10-CA

Other specified disorders of carbohydrate metabolism

Chapter IV · subcategory · degenerative * · ICD-10-CA

E749 ICD-10-CA

Disorder of carbohydrate metabolism, unspecified

Chapter IV · subcategory · degenerative * · ICD-10-CA

E750 ICD-10-CA

GM2 gangliosidosis

Chapter IV · subcategory · degenerative * · ICD-10-CA

E751 ICD-10-CA

Other gangliosidosis

Chapter IV · subcategory · degenerative * · ICD-10-CA

E752 ICD-10-CA

Other sphingolipidosis

Chapter IV · subcategory · degenerative * · ICD-10-CA

E753 ICD-10-CA

Sphingolipidosis, unspecified

Chapter IV · subcategory · degenerative * · ICD-10-CA

E754 ICD-10-CA

Neuronal ceroid lipofuscinosis

Chapter IV · subcategory · degenerative * · ICD-10-CA

E755 ICD-10-CA

Other lipid storage disorders

Chapter IV · subcategory · degenerative * · ICD-10-CA

E756 ICD-10-CA

Lipid storage disorder, unspecified

Chapter IV · subcategory · degenerative * · ICD-10-CA

E760 ICD-10-CA

Mucopolysaccharidosis, type I

Chapter IV · subcategory · degenerative * · ICD-10-CA

E761 ICD-10-CA

Mucopolysaccharidosis, type II

Chapter IV · subcategory · degenerative * · ICD-10-CA

E762 ICD-10-CA

Other mucopolysaccharidoses

Chapter IV · subcategory · degenerative * · ICD-10-CA

E763 ICD-10-CA

Mucopolysaccharidosis, unspecified

Chapter IV · subcategory · degenerative * · ICD-10-CA

E768 ICD-10-CA

Other disorders of glucosaminoglycan metabolism

Chapter IV · subcategory · degenerative * · ICD-10-CA

E769 ICD-10-CA

Disorder of glucosaminoglycan metabolism, unspecified

Chapter IV · subcategory · degenerative * · ICD-10-CA

E770 ICD-10-CA

Defects in post-translational modification of lysosomal enzymes

Chapter IV · subcategory · degenerative * · ICD-10-CA

E771 ICD-10-CA

Defects in glycoprotein degradation

Chapter IV · subcategory · degenerative * · ICD-10-CA

E778 ICD-10-CA

Other disorders of glycoprotein metabolism

Chapter IV · subcategory · degenerative * · ICD-10-CA

E779 ICD-10-CA

Disorder of glycoprotein metabolism, unspecified

Chapter IV · subcategory · degenerative * · ICD-10-CA

E780 ICD-10-CA

Pure hypercholesterolaemia

Chapter IV · subcategory · degenerative * · ICD-10-CA

E781 ICD-10-CA

Pure hyperglyceridaemia

Chapter IV · subcategory · degenerative * · ICD-10-CA

E782 ICD-10-CA

Mixed hyperlipidaemia

Chapter IV · subcategory · degenerative * · ICD-10-CA

E783 ICD-10-CA

Hyperchylomicronaemia

Chapter IV · subcategory · degenerative * · ICD-10-CA

E784 ICD-10-CA

Other hyperlipidaemia

Chapter IV · subcategory · degenerative * · ICD-10-CA

E785 ICD-10-CA

Hyperlipidaemia, unspecified

Chapter IV · subcategory · degenerative * · ICD-10-CA

E786 ICD-10-CA

Lipoprotein deficiency

Chapter IV · subcategory · degenerative * · ICD-10-CA

E788 ICD-10-CA

Other disorders of lipoprotein metabolism

Chapter IV · subcategory · degenerative * · ICD-10-CA

E789 ICD-10-CA

Disorder of lipoprotein metabolism, unspecified

Chapter IV · subcategory · degenerative * · ICD-10-CA

E790 ICD-10-CA

Hyperuricaemia without signs of inflammatory arthritis and tophaceous disease

Chapter IV · subcategory · degenerative * · ICD-10-CA

E791 ICD-10-CA

Lesch-Nyhan syndrome

Chapter IV · subcategory · degenerative * · ICD-10-CA

E798 ICD-10-CA

Other disorders of purine and pyrimidine metabolism

Chapter IV · subcategory · degenerative * · ICD-10-CA

E799 ICD-10-CA

Disorder of purine and pyrimidine metabolism, unspecified

Chapter IV · subcategory · degenerative * · ICD-10-CA

E800 ICD-10-CA

Hereditary erythropoietic porphyria

Chapter IV · subcategory · degenerative * · ICD-10-CA

E801 ICD-10-CA

Porphyria cutanea tarda

Chapter IV · subcategory · degenerative * · ICD-10-CA

E802 ICD-10-CA

Other porphyria

Chapter IV · subcategory · degenerative * · ICD-10-CA

E803 ICD-10-CA

Defects of catalase and peroxidase

Chapter IV · subcategory · degenerative * · ICD-10-CA